Respiratory Disorders in Neuromuscular Disease : Management and Practice Principles

Over the years, the life expectancy of patients with neuromuscular disease has improved thanks to new knowledge and technological innovations. This new book is entirely dedicated to the knowledge of the complex and unique profile of patients suffering from neuromuscular pathology. Many key points are discussed by specialists dedicated to neuromuscular patient care. Respiratory support is often indispensable to sustain the patient''s life. Non-invasive ventilation (NIV) has taken on an increasingly important role in the care of patients with chronic respiratory failure secondary to neuromuscular disease. The NIV approach and complementary techniques are described. The management of airways and clearance of secretions are important aspects which are dealt with in a dedicated session, and a new theme - laryngeal response pattern during NIV and cough assist techniques - is also addressed. The timing of the tracheostomy and choice of cannula are decisive in the management of the neuromuscular patient, thus the use of invasive mechanical ventilation. Topics of interest also include perioperative respiratory management, weaning from mechanical ventilation and extubation. The use of imaging techniques, such as videofluoroscopy of swallowing and sonography can support the clinician in the diagnosis of complications. Today, even pulmonary rehabilitation is an integral and indispensable part of patient care. The text - developed with the contribution of experts dedicated to the daily care of patients with neuromuscular disorders -- is an ambitious project which aims to provide an extensive discussion of the topic and support for those who already work with this type of patient, as well as for those who are starting to engage in this type of patient care.